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Disease Dentinogenesis Imperfecta

Name Dentinogenesis Imperfecta
Synonyms Capdepont Teeth | Dentinogenesis Imperfecta 1 | Dentinogenesis Imperfecta, Shields Type 2 | Dentinogenesis Imperfecta, Shields Type II | Dentinogenesis Imperfecta without Osteogenesis Imperfecta | Dentin, Opalescent | DGI1 | DGI-II | Hereditary Opalescent Dentin | Imperfecta 1, Dentinogenesis | Imperfecta, Dentinogenesis | Opalescent Dentin | Opalescent Dentin, Hereditary | Opalescent Teeth without Osteogenesis Imperfecta | Teeth, Capdepont
Definition An autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth. The dentin develops poorly with low mineral content while the pulp canal is obliterated.
Categories Congenital abnormality | Mouth disease
MeSH® ID D003811
OMIM® ID 125490
External Links
DO
DOID:4154

Top ↑ Ancestors

1. Diseases ← Stomatognathic Diseases Has associated chemicals Has associated genes Has associated exposure references ← Stomatognathic System Abnormalities Has associated chemicals Has associated genes Has associated exposure references ← Tooth Abnormalities Has associated chemicals Has associated genes ← Dentinogenesis Imperfecta Has associated chemicals Has associated genes
2. Diseases ← Stomatognathic Diseases Has associated chemicals Has associated genes Has associated exposure references ← Tooth Diseases Has associated chemicals Has associated genes Has associated exposure references ← Tooth Abnormalities Has associated chemicals Has associated genes ← Dentinogenesis Imperfecta Has associated chemicals Has associated genes
3. Diseases ← Congenital, Hereditary, and Neonatal Diseases and Abnormalities Has associated chemicals Has associated genes Has associated exposure references ← Congenital Abnormalities Has associated chemicals Has associated genes Has associated exposure references ← Stomatognathic System Abnormalities Has associated chemicals Has associated genes Has associated exposure references ← Tooth Abnormalities Has associated chemicals Has associated genes ← Dentinogenesis Imperfecta Has associated chemicals Has associated genes

Top ↑ Descendants

Dentinogenesis Imperfecta Has associated chemicals Has associated genes
  Cortical Defects, Wormian Bones, and Dentinogenesis Imperfecta
  Deafness, Autosomal Dominant 39, with Dentinogenesis Imperfecta 1 Has associated chemicals Has associated genes
  Dentinogenesis imperfecta, shields type 3 Has associated chemicals Has associated genes
  Osteogenesis imperfecta, type 1A
  Osteogenesis Imperfecta with Opalescent Teeth, Blue Sclerae and Wormian Bones, but Without Fractures
  Spondylometaphyseal dysplasia with dentinogenesis imperfecta