Skip navigation

Disease Hearing Loss, Central

Name Hearing Loss, Central
Synonyms Central Hearing Loss | Cortical Deafness | Deafness, Cortical
Definition Hearing loss due to disease of the AUDITORY PATHWAYS (in the CENTRAL NERVOUS SYSTEM) which originate in the COCHLEAR NUCLEI of the PONS and then ascend bilaterally to the MIDBRAIN, the THALAMUS, and then the AUDITORY CORTEX in the TEMPORAL LOBE. Bilateral lesions of the auditory pathways are usually required to cause central hearing loss. Cortical deafness refers to loss of hearing due to bilateral auditory cortex lesions. Unilateral BRAIN STEM lesions involving the cochlear nuclei may result in unilateral hearing loss.
Categories Ear-nose-throat disease | Nervous system disease | Signs and symptoms
MeSH® ID D006313
External Links

Top ↑ Ancestors

1. DiseasesOtorhinolaryngologic Diseases Has associated chemicals Has associated genes Has associated exposure references Ear Diseases Has associated chemicals Has associated genes Has associated exposure references Hearing Disorders Has associated chemicals Has associated genes Has associated exposure references Hearing Loss Has associated chemicals Has associated genes Has associated exposure references Hearing Loss, Sensorineural Has associated chemicals Has associated genes Hearing Loss, Central Has associated chemicals Has associated genes
2. DiseasesOtorhinolaryngologic Diseases Has associated chemicals Has associated genes Has associated exposure references Ear Diseases Has associated chemicals Has associated genes Has associated exposure references Retrocochlear Diseases Has associated chemicals Has associated genes Has associated exposure references Auditory Diseases, Central Has associated chemicals Has associated genes Hearing Loss, Central Has associated chemicals Has associated genes
3. DiseasesNervous System Diseases Has associated chemicals Has associated genes Has associated exposure references Central Nervous System Diseases Has associated chemicals Has associated genes Has associated exposure references Brain Diseases Has associated chemicals Has associated genes Has associated exposure references Auditory Diseases, Central Has associated chemicals Has associated genes Hearing Loss, Central Has associated chemicals Has associated genes
4. DiseasesNervous System Diseases Has associated chemicals Has associated genes Has associated exposure references Neurologic Manifestations Has associated chemicals Has associated genes Has associated exposure references Sensation Disorders Has associated chemicals Has associated genes Has associated exposure references Hearing Disorders Has associated chemicals Has associated genes Has associated exposure references Hearing Loss Has associated chemicals Has associated genes Has associated exposure references Hearing Loss, Sensorineural Has associated chemicals Has associated genes Hearing Loss, Central Has associated chemicals Has associated genes
5. DiseasesPathological Conditions, Signs and Symptoms Has associated chemicals Has associated genes Has associated exposure references Signs and Symptoms Has associated chemicals Has associated genes Has associated exposure references Neurologic Manifestations Has associated chemicals Has associated genes Has associated exposure references Sensation Disorders Has associated chemicals Has associated genes Has associated exposure references Hearing Disorders Has associated chemicals Has associated genes Has associated exposure references Hearing Loss Has associated chemicals Has associated genes Has associated exposure references Hearing Loss, Sensorineural Has associated chemicals Has associated genes Hearing Loss, Central Has associated chemicals Has associated genes

Top ↑ Descendants

Hearing Loss, Central Has associated chemicals Has associated genes
  Auditory neuropathy Has associated chemicals Has associated genes
  Auditory Neuropathy, Autosomal Dominant, 1 Has associated chemicals Has associated genes
  Deafness, autosomal dominant nonsyndromic sensorineural 3
  Deafness, autosomal dominant nonsyndromic sensorineural 53
  Deafness, autosomal recessive 51
  Deafness, autosomal recessive 55
  Deafness nephritis ano rectal malformation
  Deafness, Neural, Congenital Moderate
  Deafness, neurosensory, autosomal recessive 47
  Groll Hirschowitz syndrome
  Jensen syndrome Has associated chemicals Has associated genes
  Mitochondrial myopathy with lactic acidosis Has associated chemicals Has associated genes
  Optic atrophy polyneuropathy deafness Has associated chemicals Has associated genes
  Ruzicka Goerz Anton syndrome
  Santos Mateus Leal syndrome
  Thumb, Hypoplastic, with Choroid Coloboma, Poorly Developed Antihelix, and Deafness