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Disease Bulbar Palsy, Progressive

Name Bulbar Palsy, Progressive
Synonyms Bulbar Palsies | Bulbar Palsies, Progressive | Bulbar Palsy | Bulbar Palsy, Progressive, Of Childhood | Bulbar Paralyses | Bulbar Paralysis | Childhood Progressive Bulbar Palsy | Fazio-Londe Disease | Fazio Londe Syndrome | Fazio-Londe Syndrome | Palsies, Bulbar | Palsies, Progressive Bulbar | Palsy, Bulbar | Palsy, Progressive Bulbar | Paralysis, Bulbar | Progressive Bulbar Palsies | Progressive Bulbar Palsy | Progressive Bulbar Palsy of Childhood | Syndrome, Fazio-Londe
Definition A motor neuron disease marked by progressive weakness of the muscles innervated by cranial nerves of the lower brain stem. Clinical manifestations include dysarthria, dysphagia, facial weakness, tongue weakness, and fasciculations of the tongue and facial muscles. The adult form of the disease is marked initially by bulbar weakness which progresses to involve motor neurons throughout the neuroaxis. Eventually this condition may become indistinguishable from AMYOTROPHIC LATERAL SCLEROSIS. Fazio-Londe syndrome is an inherited form of this illness which occurs in children and young adults. (Adams et al., Principles of Neurology, 6th ed, p1091; Brain 1992 Dec;115(Pt 6):1889-1900)
Categories Nervous system disease
MeSH® ID D010244
OMIM® ID 211500
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Top ↑ Ancestors

1. DiseasesNervous System Diseases Has associated chemicals Has associated genes Has associated exposure references Neurodegenerative Diseases Has associated chemicals Has associated genes Has associated exposure references Motor Neuron Disease Has associated chemicals Has associated genes Has associated exposure references Bulbar Palsy, Progressive Has associated chemicals Has associated genes
2. DiseasesNervous System Diseases Has associated chemicals Has associated genes Has associated exposure references Neuromuscular Diseases Has associated chemicals Has associated genes Has associated exposure references Motor Neuron Disease Has associated chemicals Has associated genes Has associated exposure references Bulbar Palsy, Progressive Has associated chemicals Has associated genes

Top ↑ Descendants

Bulbar Palsy, Progressive Has associated chemicals Has associated genes
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