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Disease Caroli Disease

Name Caroli Disease
Synonyms Caroli's Disease | Carolis Disease | Caroli's Syndrome | Carolis Syndrome | Caroli Syndrome | Disease, Caroli | Disease, Caroli's | Syndrome, Caroli's
Definition Congenital cystic dilatation of the intrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC). It consists of 2 types: simple Caroli disease is characterized by bile duct dilatation (ectasia) alone; and complex Caroli disease is characterized by bile duct dilatation with extensive hepatic fibrosis and portal hypertension (HYPERTENSION, PORTAL). Benign renal tubular ectasia is associated with both types of Caroli disease.
Categories Congenital abnormality | Digestive system disease | Genetic disease (inborn)
MeSH® ID D016767
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1. DiseasesDigestive System Diseases Has associated chemicals Has associated genes Has associated exposure references Biliary Tract Diseases Has associated chemicals Has associated genes Has associated exposure references Bile Duct Diseases Has associated chemicals Has associated genes Has associated exposure references Choledochal Cyst Has associated chemicals Has associated genes Caroli Disease
2. DiseasesDigestive System Diseases Has associated chemicals Has associated genes Has associated exposure references Digestive System Abnormalities Has associated chemicals Has associated genes Choledochal Cyst Has associated chemicals Has associated genes Caroli Disease
3. DiseasesCongenital, Hereditary, and Neonatal Diseases and Abnormalities Has associated chemicals Has associated genes Has associated exposure references Congenital Abnormalities Has associated chemicals Has associated genes Has associated exposure references Abnormalities, Multiple Has associated chemicals Has associated genes Ciliopathies Has associated chemicals Has associated genes Caroli Disease
4. DiseasesCongenital, Hereditary, and Neonatal Diseases and Abnormalities Has associated chemicals Has associated genes Has associated exposure references Congenital Abnormalities Has associated chemicals Has associated genes Has associated exposure references Digestive System Abnormalities Has associated chemicals Has associated genes Choledochal Cyst Has associated chemicals Has associated genes Caroli Disease
5. DiseasesCongenital, Hereditary, and Neonatal Diseases and Abnormalities Has associated chemicals Has associated genes Has associated exposure references Genetic Diseases, Inborn Has associated chemicals Has associated genes Has associated exposure references Ciliopathies Has associated chemicals Has associated genes Caroli Disease

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Caroli Disease
  Caroli disease isolated