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Disease Dermatofibrosarcoma

Name Dermatofibrosarcoma
Synonyms Bednar's Tumor | Bednars Tumor | Bednar Tumor | Cell Fibroblastoma, Giant | Cell Fibroblastomas, Giant | Darier Ferrand Tumor | Darier-Ferrand Tumor | Darier Hoffmann Tumor | Darier-Hoffmann Tumor | Dermatofibrosarcoma Protuberan | Dermatofibrosarcoma Protuberan, Familial | Dermatofibrosarcoma Protuberan, Fibrosarcomatous | Dermatofibrosarcoma Protuberan, Giant | Dermatofibrosarcoma Protuberan, Metastatic | Dermatofibrosarcoma Protuberan, Myxoid | Dermatofibrosarcoma Protuberan, Pigmented | Dermatofibrosarcoma Protuberans | Dermatofibrosarcoma Protuberans, Familial | Dermatofibrosarcoma Protuberans, Fibrosarcomatous | Dermatofibrosarcoma Protuberans, Giant | Dermatofibrosarcoma Protuberans, Giant Cell | Dermatofibrosarcoma Protuberans, Metastatic | Dermatofibrosarcoma Protuberans, Myxoid | Dermatofibrosarcoma Protuberans, Pigmented | Dermatofibrosarcomas | DFSP | DFSP, Fibrosarcomatous | DFSP, Juvenile | DFSP, Myxoid | DFSP, Pigmented | DFSPs, Fibrosarcomatous | DFSPs, Juvenile | DFSPs, Myxoid | DFSPs, Pigmented | Familial Dermatofibrosarcoma Protuberan | Familial Dermatofibrosarcoma Protuberans | Fibroblastoma, Giant Cell | Fibroblastomas, Giant Cell | Fibrosarcomatous Dermatofibrosarcoma Protuberan | Fibrosarcomatous Dermatofibrosarcoma Protuberans | Fibrosarcomatous DFSP | Fibrosarcomatous DFSPs | FS-DFSP | Giant Cell Fibroblastoma | Giant Cell Fibroblastomas | Giant Dermatofibrosarcoma Protuberan | Giant Dermatofibrosarcoma Protuberans | Juvenile DFSP | Juvenile DFSPs | Metastatic Dermatofibrosarcoma Protuberan | Metastatic Dermatofibrosarcoma Protuberans | Myxoid Dermatofibrosarcoma Protuberan | Myxoid Dermatofibrosarcoma Protuberans | Myxoid DFSP | Myxoid DFSPs | Pigmented Dermatofibrosarcoma Protuberan | Pigmented Dermatofibrosarcoma Protuberans | Pigmented DFSP | Pigmented DFSPs | Protuberan, Dermatofibrosarcoma | Protuberan, Familial Dermatofibrosarcoma | Protuberan, Fibrosarcomatous Dermatofibrosarcoma | Protuberan, Giant Dermatofibrosarcoma | Protuberan, Metastatic Dermatofibrosarcoma | Protuberan, Myxoid Dermatofibrosarcoma | Protuberan, Pigmented Dermatofibrosarcoma | Protuberans, Dermatofibrosarcoma | Protuberans, Familial Dermatofibrosarcoma | Protuberans, Fibrosarcomatous Dermatofibrosarcoma | Protuberans, Giant Dermatofibrosarcoma | Protuberans, Metastatic Dermatofibrosarcoma | Protuberans, Myxoid Dermatofibrosarcoma | Protuberans, Pigmented Dermatofibrosarcoma | Tumor, Bednar | Tumor, Bednar's | Tumor, Darier-Ferrand | Tumor, Darier-Hoffmann
Definition A sarcoma of the deep layers of the skin. The tumors are locally aggressive tends to recur but rarely metastatic. It can be classified into variants depending on the cell type tumors are derived from or by its characteristics: Pigmented variant from MELANIN-containing DERMAL DENDRITIC CELLS; Myxoid variant, myxoid STROMAL CELLS; Giant cell variant characterized by GIANT CELLS in the tumors; and Fibrosarcomatous variant chracterized by tumor areas histologically indistinguishable from FIBROSARCOMA.
Categories Cancer
MeSH® ID D018223
OMIM® ID 607907
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Top ↑ Ancestors

1. DiseasesNeoplasms Has associated chemicals Has associated genes Has associated exposure references Neoplasms by Histologic Type Has associated chemicals Has associated genes Has associated exposure references Neoplasms, Connective and Soft Tissue Has associated chemicals Has associated genes Has associated exposure references Neoplasms, Connective Tissue Has associated chemicals Has associated genes Neoplasms, Fibrous Tissue Has associated chemicals Has associated genes Fibrosarcoma Has associated chemicals Has associated genes Dermatofibrosarcoma Has associated chemicals Has associated genes
2. DiseasesNeoplasms Has associated chemicals Has associated genes Has associated exposure references Neoplasms by Histologic Type Has associated chemicals Has associated genes Has associated exposure references Neoplasms, Connective and Soft Tissue Has associated chemicals Has associated genes Has associated exposure references Sarcoma Has associated chemicals Has associated genes Has associated exposure references Fibrosarcoma Has associated chemicals Has associated genes Dermatofibrosarcoma Has associated chemicals Has associated genes

Top ↑ Descendants

None.