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Disease Neurofibrosarcoma

Name Neurofibrosarcoma
Synonyms Neurofibrosarcomas | Neurogenic Sarcoma | Neurogenic Sarcomas | Sarcoma, Neurogenic | Sarcomas, Neurogenic
Definition A malignant tumor that arises from small cutaneous nerves, is locally aggressive, and has a potential for metastasis. Characteristic histopathologic features include proliferating atypical spindle cells with slender wavy and pointed nuclei, hypocellular areas, and areas featuring organized whorls of fibroblastic proliferation. The most common primary sites are the extremities, retroperitoneum, and trunk. These tumors tend to present in childhood, often in association with NEUROFIBROMATOSIS 1. (From DeVita et al., Cancer: Principles & Practice of Oncology, 5th ed, p1662; Mayo Clin Proc 1990 Feb;65(2):164-72)
Categories Cancer | Nervous system disease
MeSH® ID D018319
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1. DiseasesNeoplasms Has associated chemicals Has associated genes Has associated exposure references Neoplasms by Histologic Type Has associated chemicals Has associated genes Has associated exposure references Neoplasms, Connective and Soft Tissue Has associated chemicals Has associated genes Has associated exposure references Neoplasms, Connective Tissue Has associated chemicals Has associated genes Neoplasms, Fibrous Tissue Has associated chemicals Has associated genes Fibrosarcoma Has associated chemicals Has associated genes Neurofibrosarcoma Has associated chemicals Has associated genes
2. DiseasesNeoplasms Has associated chemicals Has associated genes Has associated exposure references Neoplasms by Histologic Type Has associated chemicals Has associated genes Has associated exposure references Neoplasms, Connective and Soft Tissue Has associated chemicals Has associated genes Has associated exposure references Sarcoma Has associated chemicals Has associated genes Has associated exposure references Fibrosarcoma Has associated chemicals Has associated genes Neurofibrosarcoma Has associated chemicals Has associated genes
3. DiseasesNeoplasms Has associated chemicals Has associated genes Has associated exposure references Neoplasms by Histologic Type Has associated chemicals Has associated genes Has associated exposure references Neoplasms, Nerve Tissue Has associated chemicals Has associated genes Has associated exposure references Nerve Sheath Neoplasms Has associated chemicals Has associated genes Has associated exposure references Neurofibroma Has associated chemicals Has associated genes Neurofibrosarcoma Has associated chemicals Has associated genes
4. DiseasesNervous System Diseases Has associated chemicals Has associated genes Has associated exposure references Nervous System Neoplasms Has associated chemicals Has associated genes Has associated exposure references Peripheral Nervous System Neoplasms Has associated chemicals Has associated genes Has associated exposure references Nerve Sheath Neoplasms Has associated chemicals Has associated genes Has associated exposure references Neurofibroma Has associated chemicals Has associated genes Neurofibrosarcoma Has associated chemicals Has associated genes
5. DiseasesNervous System Diseases Has associated chemicals Has associated genes Has associated exposure references Neuromuscular Diseases Has associated chemicals Has associated genes Has associated exposure references Peripheral Nervous System Diseases Has associated chemicals Has associated genes Peripheral Nervous System Neoplasms Has associated chemicals Has associated genes Has associated exposure references Nerve Sheath Neoplasms Has associated chemicals Has associated genes Has associated exposure references Neurofibroma Has associated chemicals Has associated genes Neurofibrosarcoma Has associated chemicals Has associated genes

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