Skip navigation

Disease Hemangioblastoma

Name Hemangioblastoma
Synonyms Hemangioblastoma, Multiple | Hemangioblastomas | Hemangioblastomas, Multiple | Multiple Hemangioblastoma | Multiple Hemangioblastomas
Definition A benign tumor of the nervous system that may occur sporadically or in association with VON HIPPEL-LINDAU DISEASE. It accounts for approximately 2% of intracranial tumors, arising most frequently in the cerebellar hemispheres and vermis. Histologically, the tumors are composed of multiple capillary and sinusoidal channels lined with endothelial cells and clusters of lipid-laden pseudoxanthoma cells. Usually solitary, these tumors can be multiple and may also occur in the brain stem, spinal cord, retina, and supratentorial compartment. Cerebellar hemangioblastomas usually present in the third decade with INTRACRANIAL HYPERTENSION, and ataxia. (From DeVita et al., Cancer: Principles and Practice of Oncology, 5th ed, pp2071-2)
Categories Cancer
MeSH® ID D018325
External Links

Top ↑ Ancestors

DiseasesNeoplasms Has associated chemicals Has associated genes Has associated exposure references Neoplasms by Histologic Type Has associated chemicals Has associated genes Has associated exposure references Neoplasms, Vascular Tissue Has associated chemicals Has associated genes Has associated exposure references Hemangioma Has associated chemicals Has associated genes Hemangioma, Capillary Has associated chemicals Has associated genes Hemangioblastoma Has associated chemicals Has associated genes

Top ↑ Descendants

None.