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Disease Erdheim-Chester Disease

Name Erdheim-Chester Disease
Synonyms Erdheim Chester Disease | Granulomatosis, Lipid | Lipid Granulomatosis
Definition A rare form of non-Langerhans-cell histiocytosis (HISTIOCYTOSIS, NON-LANGERHANS-CELL) with onset in middle age. The systemic disease is characterized by infiltration of lipid-laden macrophages, multinucleated giant cells, an inflammatory infiltrate of lymphocytes and histiocytes in the bone marrow, and a generalized sclerosis of the long bones.
Categories Lymphatic disease
MeSH® ID D031249
External Links

Top ↑ Ancestors

DiseasesHemic and Lymphatic Diseases Has associated chemicals Has associated genes Has associated exposure references Lymphatic Diseases Has associated chemicals Has associated genes Has associated exposure references Histiocytosis Has associated chemicals Has associated genes Histiocytosis, Non-Langerhans-Cell Has associated chemicals Has associated genes Erdheim-Chester Disease

Top ↑ Descendants

None.