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Disease Idiopathic Pulmonary Fibrosis

Name Idiopathic Pulmonary Fibrosis
Synonyms Cryptogenic Fibrosing Alveolitides | Cryptogenic Fibrosing Alveolitis | Disease, Hamman-Rich | Diseases, Hamman-Rich | Dysplasia, Fibrocystic Pulmonary | Dysplasias, Fibrocystic Pulmonary | Familial Idiopathic Pulmonary Fibrosis | Fibrocystic Pulmonary Dysplasia | Fibrocystic Pulmonary Dysplasias | Fibrosing Alveolitides, Cryptogenic | Fibrosing Alveolitis, Cryptogenic | Hamman Rich Disease | Hamman-Rich Disease | Hamman-Rich Diseases | Idiopathic Fibrosing Alveolitis, Chronic Form | Idiopathic Pulmonary Fibroses | Idiopathic Pulmonary Fibrosis, Familial | Interstitial Pneumonias, Usual | Interstitial Pneumonia, Usual | Interstitial Pneumonitides, Usual | Interstitial Pneumonitis, Usual | INTERSTITIAL PNEUMONITIS, USUAL;UIP HAMMAN-RICH DISEASE, INCLUDED | IPF | Pneumonitides, Usual Interstitial | Pneumonitis, Usual Interstitial | Pulmonary Dysplasia, Fibrocystic | Pulmonary Dysplasias, Fibrocystic | Pulmonary Fibroses, Idiopathic | Pulmonary Fibrosis, Idiopathic | Usual Interstitial Pneumonia | Usual Interstitial Pneumonias | Usual Interstitial Pneumonitides | Usual Interstitial Pneumonitis
Definition A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.
Categories Respiratory tract disease
MeSH® ID D054990
OMIM® ID 178500
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Top ↑ Ancestors

1. DiseasesRespiratory Tract Diseases Has associated chemicals Has associated genes Has associated exposure references Lung Diseases Has associated chemicals Has associated genes Has associated exposure references Lung Diseases, Interstitial Has associated chemicals Has associated genes Has associated exposure references Idiopathic Interstitial Pneumonias Has associated chemicals Has associated genes Idiopathic Pulmonary Fibrosis Has associated chemicals Has associated genes
2. DiseasesRespiratory Tract Diseases Has associated chemicals Has associated genes Has associated exposure references Lung Diseases Has associated chemicals Has associated genes Has associated exposure references Pulmonary Fibrosis Has associated chemicals Has associated genes Has associated exposure references Idiopathic Pulmonary Fibrosis Has associated chemicals Has associated genes

Top ↑ Descendants

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