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Disease Isolated Noncompaction of the Ventricular Myocardium

Name Isolated Noncompaction of the Ventricular Myocardium
Synonyms Isolated Noncompaction of the Left Ventricular Myocardium, X-Linked | Isolated Non-compaction of the Ventricular Myocardium | Noncompaction of the Left Ventricular Myocardium, Autosomal Dominant
Definition Rare congenital cardiomyopathies characterized by the lack of left ventricular myocardium compaction. The noncompaction results in numerous prominent trabeculations and a loose myocardial meshwork (spongy myocardium) in the LEFT VENTRICLE. Heterogeneous clinical features include diminished systolic function sometimes associated with left ventricular dilation, that presents either neonatally or progressively. Often, the RIGHT VENTRICLE is also affected. CONGESTIVE HEART FAILURE; PULMONARY EMBOLISM; and ventricular ARRHYTHMIA are commonly seen.
Categories Cardiovascular disease | Congenital abnormality | Genetic disease (inborn)
MeSH® ID D056830

Top ↑ Ancestors

1. DiseasesCardiovascular Diseases Has associated chemicals Has associated genes Has associated exposure references Cardiovascular Abnormalities Has associated chemicals Has associated genes Has associated exposure references Heart Defects, Congenital Has associated chemicals Has associated genes Has associated exposure references Isolated Noncompaction of the Ventricular Myocardium Has associated chemicals Has associated genes
2. DiseasesCardiovascular Diseases Has associated chemicals Has associated genes Has associated exposure references Heart Diseases Has associated chemicals Has associated genes Has associated exposure references Cardiomyopathies Has associated chemicals Has associated genes Endocardial Fibroelastosis Has associated chemicals Has associated genes Isolated Noncompaction of the Ventricular Myocardium Has associated chemicals Has associated genes
3. DiseasesCardiovascular Diseases Has associated chemicals Has associated genes Has associated exposure references Heart Diseases Has associated chemicals Has associated genes Has associated exposure references Heart Defects, Congenital Has associated chemicals Has associated genes Has associated exposure references Isolated Noncompaction of the Ventricular Myocardium Has associated chemicals Has associated genes
4. DiseasesCongenital, Hereditary, and Neonatal Diseases and Abnormalities Has associated chemicals Has associated genes Has associated exposure references Congenital Abnormalities Has associated chemicals Has associated genes Has associated exposure references Abnormalities, Multiple Has associated chemicals Has associated genes Isolated Noncompaction of the Ventricular Myocardium Has associated chemicals Has associated genes
5. DiseasesCongenital, Hereditary, and Neonatal Diseases and Abnormalities Has associated chemicals Has associated genes Has associated exposure references Congenital Abnormalities Has associated chemicals Has associated genes Has associated exposure references Cardiovascular Abnormalities Has associated chemicals Has associated genes Has associated exposure references Heart Defects, Congenital Has associated chemicals Has associated genes Has associated exposure references Isolated Noncompaction of the Ventricular Myocardium Has associated chemicals Has associated genes
6. DiseasesCongenital, Hereditary, and Neonatal Diseases and Abnormalities Has associated chemicals Has associated genes Has associated exposure references Genetic Diseases, Inborn Has associated chemicals Has associated genes Has associated exposure references Genetic Diseases, X-Linked Has associated chemicals Has associated genes Isolated Noncompaction of the Ventricular Myocardium Has associated chemicals Has associated genes

Top ↑ Descendants

Isolated Noncompaction of the Ventricular Myocardium Has associated chemicals Has associated genes
  Cardiomyopathy, Dilated, with Left Ventricular Noncompaction
  LEFT VENTRICULAR NONCOMPACTION 1 Has associated chemicals Has associated genes
  LEFT VENTRICULAR NONCOMPACTION 2
  Noncompaction of Left Ventricular Myocardium, Familial Isolated, Autosomal Dominant 1
  Noncompaction of Left Ventricular Myocardium, Familial Isolated, Autosomal Dominant 2